Archives of Head and Neck Surgery
https://archivesheadnecksurgery.com/article/doi/10.4322/ahns.2021.0005
Archives of Head and Neck Surgery
Case Report Tumors of the lip and oral cavity

Ectopic palatine tonsil meningioma in type 2 neurofibromatosis: a few times documented phenomenon

Juan Miguel Alemán-Iñiguez, Christian Valencia Padilla

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Abstract

Type 2 neurofibromatosis is a hereditary neurocutaneous entity, characterized by associations with cranial and spinal meningiomas; extra neural cases are infrequent. There are oral meningiomas reports, however their presence at the palatine tonsils have not been described. This is a patient, with type 2 neurofibromatosis inherited from her father. The guest, presented progressive odyno-dysphagia whose etiology was WHO I meningioma in palatine tonsils, while the cranial image showed same lineage meningiomas that were surgically treated. This rare phenomenon in the context of an uncommon disease and the events that would explain the arrival of menigiomatous tissue to the palate are discussed.

Keywords

meningioma; neurofibromatosis 2; palatine tonsil.

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Submitted date:
07/08/2021

Accepted date:
07/31/2021

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